ID | 31823 |
JaLCDOI | |
FullText URL | |
Author |
Nakanishi, Kazuo
Sugimoto, Yoshihisa
Misawa, Haruo
Takigawa, Tomoyuki
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Abstract | Scoliosis is a common clinical manifestation of Rett syndrome, a neurodevelopmental disorder that almost exclusively affects females. The spinal curve in patients with Rett syndrome is typically a long C curve of a neuromuscular type. As the onset of the scoliosis is very early and shows rapid progression, early surgical intervention has been recommended to prevent a life-threatening collapsing spine syndrome. However, there are high perioperative risks in Rett syndrome patients who undergo spinal surgery, such as neurological compromise and respiratory dysfunction due to rigid spinal curve. We herein report the surgical result of treating severe rapid progressive thoracic scoliosis in a 16-year-old girl with Rett syndrome. Posterior segmental pedicle screw fixation was performed from T1 to L3 using a computer-assisted technique. Post-operative radiography demonstrated a good correction of the curve in both the sagittal and coronal alignment. There were no postoperative complications such as neurological compromise. The patient had maintained satisfactory spinal balance as of the 3-year follow-up examination. |
Keywords | Rett syndrome
scoliosis
computer navigation-assisted surgery
segmental pedicle screw fixation
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Amo Type | Case Report
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Publication Title |
Acta Medica Okayama
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Published Date | 2009-12
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Volume | volume63
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Issue | issue6
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Publisher | Okayama University Medical School
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Start Page | 373
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End Page | 377
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ISSN | 0386-300X
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NCID | AA00508441
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Content Type |
Journal Article
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language |
English
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File Version | publisher
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Refereed |
True
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PubMed ID | |
Web of Science KeyUT |