ID | 31823 |
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フルテキストURL | |
著者 |
Tanaka, Masato
Department of Orthopaedic Surgery, Okayama University Hospital
ORCID
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publons
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Nakanishi, Kazuo
Department of Orthopaedic Surgery, Okayama University Hospital
Sugimoto, Yoshihisa
Department of Orthopaedic Surgery, Okayama University Hospital
Misawa, Haruo
Department of Orthopaedic Surgery, Okayama University Hospital
Takigawa, Tomoyuki
Department of Orthopaedic Surgery, Okayama University Hospital
Nishida, Keiichiro
Department of Human Morphology, Okayama University Graduate School of Medicine, Dentistry and Pharmaceutical Sciences
Kaken ID
publons
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Ozaki, Toshifumi
Department of Orthopaedic Surgery, Okayama University Hospital
Kaken ID
publons
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抄録 | Scoliosis is a common clinical manifestation of Rett syndrome, a neurodevelopmental disorder that almost exclusively affects females. The spinal curve in patients with Rett syndrome is typically a long C curve of a neuromuscular type. As the onset of the scoliosis is very early and shows rapid progression, early surgical intervention has been recommended to prevent a life-threatening collapsing spine syndrome. However, there are high perioperative risks in Rett syndrome patients who undergo spinal surgery, such as neurological compromise and respiratory dysfunction due to rigid spinal curve. We herein report the surgical result of treating severe rapid progressive thoracic scoliosis in a 16-year-old girl with Rett syndrome. Posterior segmental pedicle screw fixation was performed from T1 to L3 using a computer-assisted technique. Post-operative radiography demonstrated a good correction of the curve in both the sagittal and coronal alignment. There were no postoperative complications such as neurological compromise. The patient had maintained satisfactory spinal balance as of the 3-year follow-up examination. |
キーワード | Rett syndrome
scoliosis
computer navigation-assisted surgery
segmental pedicle screw fixation
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Amo Type | Case Report
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出版物タイトル |
Acta Medica Okayama
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発行日 | 2009-12
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巻 | 63巻
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号 | 6号
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出版者 | Okayama University Medical School
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開始ページ | 373
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終了ページ | 377
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ISSN | 0386-300X
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NCID | AA00508441
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資料タイプ |
学術雑誌論文
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言語 |
英語
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論文のバージョン | publisher
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査読 |
有り
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