JaLCDOI 10.18926/AMO/56077
FullText URL 72_3_301.pdf
Author Kakio, Yuki| A. Uchida, Haruhito| Kitagawa, Masashi| Arata, Yuka| Kato, Ayako| Inoue-Torii, Akiko| Hinamoto, Norikazu| Ogawa-Akiyama, Ayu| Sugiyama, Hitoshi| Wada, Jun|
Abstract Renal involvement is occasionally observed in Wiskott-Aldrich syndrome (WAS) and X-linked thrombocytopenia (XLT). It has been reported that galactose-deficient IgA is a closely linked to IgA nephropathy (IgAN), suggesting that patients with XLT/WAS associated with reduced galactosylation on serum IgA are susceptible to IgAN. It is necessary to pay more attention to patients with IgAN due to the potential complication with XLT/WAS. We here present a patient of XLT complicated with mild IgAN who underwent tonsillectomy combined with steroid pulse therapy to achieve complete clinical remission.
Keywords IgAN nephropathy Wiskott-Aldrich syndrome X-linked thrombocytopenia galactose-deficient IgA1
Amo Type Case Report
Published Date 2018-06
Publication Title Acta Medica Okayama
Volume volume72
Issue issue3
Publisher Okayama University Medical School
Start Page 301
End Page 307
ISSN 0386-300X
NCID AA00508441
Content Type Journal Article
language 英語
Copyright Holders CopyrightⒸ 2018 by Okayama University Medical School
File Version publisher
Refereed True
PubMed ID 29926009